Urologie pro praxi 4/2022

Zinner syndrome: case report

Zinner syndrome is a rare congenital anomaly of Wolffian duct consisting of unilateral renal agenesis, ipsilateral seminal vesicle cysts and ejaculatory duct obstruction. The diagnosis is usually established at the age of increased sexual activity (adults, adolescents). Patients with this diagnosis have fertility problems as a result of ejaculatory duct obstruction. We present a case of a boy followed in our department since birth for right renal multicystic dysplasia diagnosed prenatally. At the age of 20 months a resorption of dysplastic kidney was detected and the boy was followed as a patients with a solitary kidney. At the age of 15 years a retrovesical multilocular mass was discovered on ultrasound. Magnetic resonance imaging of abdomen and pelvis revealed cystic dilatation of seminal vesicle and the diagnosis was established.

Keywords: Zinner syndrome, anomaly of Wolfian duct, infertility, multicystic renal dysplasia, seminal vesicle cyst.