Urologie pro praxi 3/2023

Metastatic/multicentric renal epithelioid angiomyolipoma – clinical case report

Renal epithelioid angiomyolipoma (ReAML) is a rare subtype of angiomyolipoma. It is a benign kidney disease, in which cases of aggressive behavior and malignancy have been reported. These tumors represent 8% of operated kidney angiomyolipomas. Diagnosis is based on histological findings. The aim of this text is to review the information on this issue, the histological picture and the case report of a 42-year-old woman operated at our department who was found to have multicentric or metastatic involvement of the retroperitoneal lymph node.

Keywords: renal epithelioid angiomyolipoma, PECom, cathepsin K, mTOR.