Neurológia pre prax 5/2017

Stevens-Johnson syndrome: complications as part of neurointensive care

Stevens-Johnson syndrome (SJS) is a rare disease with an immunopathological background, most frequently occurring in association with a medication administered. The disease is characterized by skin manifestations, specifically maculopapular exanthema, blisters, and large skin defects. Skin signs are accompanied by general ones (temperature, anaemia, leukopenia, hypoalbuminaemia). The mortality is high, with patients most commonly dying from infectious complications. We present a case of a female patient who developed SJS as part of neurointensive care. The aim of this case report is to introduce this rare syndrome to neurological professionals.

Keywords: Stevens-Johnson syndrome, toxic epidermal necrolysis, Lyell’s syndrome, neurointensive care, non-convulsive status epilepticus